Abstract

Dr. Swagata Dowerah, Dr. Rashmi Deori and *Dr. Kaustubhmoni Gogoi

ABSTRACT

Introduction: Teratomas belong to a class of tumors known as nonseminomatous germ cell tumors occurring in a decreasing order of frequency in ovary, testis, mediastinum and retroperitoneum. We present a case of primary retroperitoneal teratoma occurring in a child of 1 year 8 months which was successfully resected along with review of literature. Case report: A 1 year 8 month old boy male presented to the pediatric surgery OPD with a lump in the abdomen. The patient was operated upon by the pediatric surgeon and specimen was sent for histopathological examination. On gross examination, a soft tissue specimen measuring 17x12x5cms was noted which was multicystic, grayish-white in colour. Upon cut section, the specimen was multiloculated with solid and cystic parts. The cysts contained sebaceous material. There was also presence of hair arising from within the solid and the cystic parts. On microscopic examination different areas showed presence of a normal looking stratified squamous epithelium mostly and pseudostrafied ciliated columnar epithelium at a few places. The subepithelium contained a few clusters of acinar looking glandular structures along with presence of mature looking sebaceous glands, hair follicles. Immature neuroectodermal components were not seen. The picture was consistent with mature cystic teratoma. Conclusion: Retroperitoneal teratomas are uncommon tumors and mostly benign. The most important factor in the treatment of these tumors is complete surgical resection of the tumor which offers an excellent prognosis.